The authors describe a patient who presented from birth on a severe involvement of connective tissues with pathological fractures, lack of auricular cartilage, hyperlaxity of fingers and cutis laxa with deep folds, all suggestive of derangements of collagen and elastin. Hypothermia at 24 hours of age should have already indicated the possibility of Menkes' syndrome. From the 3rd month on, the pati

Sleep disordered breathing (SDB) including obstructive and central sleep apnoea/ hypopnoea as well as periodic breathing (PB) is common and is believed to increase risk for mortality in patients with congestive heart failure (CHF). Mandibular advancement device (MAD) has widely been recommended for treatment of obstructive sleep apnoea but the method has never been investigated for treatment of SD

Non-linearity in the energy response of a Si p-i-n charged particle detector has been studied for incident particles with Z(1) between 3 and 26, and energies between 0.1 and 0.7 MeV per nucleon. Although the data closely followed a straight line relations, fitting of the data to a third order polynomial revealed that the response exhibited a persistent curvature that acted to reduce the energy int

Romania has for a long time been lacking good palaeoenvironmental records, particularly for the Late Quaternary. A chronological framework had been nearly absent and the vegetation development had been reconstructed entirely from pollen data. Data sets from this part of Europe are important for assessing the spatial variability of past vegetation and climatic changes and to reconstruct tree migrat

In this report we present an extension of the pooled analysis of the prognostic impact of urokinase-type plasminogen activator (uPA) and its inhibitor PAI-I in breast cancer patients. We analyzed a different endpoint, metastasis-free survival (MFS). We checked the consistency of the estimates for uPA and PAI-I for relapse-free survival (RFS) and MFS exploring possible sources of heterogeneity. Nod

In his fetishist argument, Michael Smith raises an important question: What is the content of the motivational states that constitute moral motivation? Although the argument has been widely discussed, this question has not received the attention it deserves. In the present paper, I use Smith's argument as a point of departure for a discussion of how advocates of externalism as regards moral judgem

Study Design. Experimental study. Objectives. To compare two devices for measuring cervical range of motion, a three-dimensional ultrasound motion device (Zebris) and a gravity-reference goniometer (Myrin). Summary of Background Data. Assessment of cervical range of motion is used to evaluate the effect of different treatments, determine impairment, and ascertain the relationship between neck diso

Evidence-based practice presupposes evidence-based decision-making. In the debate it is argued that a social work fashioned after evidence should be more rational, less authoritarian and built on scientific knowledge, respect and ethics. Yet the empirical evidence that this idea works is weak. In fact the difficulties met during efforts to implement evidence could be a sound reaction. Indeed diffi

Popular Abstract in Swedish De flesta samhällsvetarna har betrakat de fattiga i utvecklingsländerna as marginella perse: de saknar de psykologiska förutsättningarna för att handla rationellt. Med min avhandling vill jag argumentera mot detta perspektiv. Jag göt det genom att bevisa att deras handlingar är rationella; de måste ta itu med ekonomiska, sociala, politiska och kulturella hinder som härmIn the present doctoral dissertation an attempt is made to qualify the theorertical assumptions about the marginal characret of the popular sectors of the developing countries. According to these theories, individuals belonging to the populart sectors cannot become fully members of their societies because they lack the attitudinal prerequisites. My argument is that their actions are quite sophisti

This article addresses two main questions both of which are raised by Risto Nurmela’s comparison between Judaism and Christianity, the first being the statement that Christology ”of course” is the dividing line between the two religions. This assertion must be refined in order to be applicable since (1) it gives vent to only one of two perspectives (i.e. it articulates only the Christian position)

The effect of bioaugmentation with an anaerobic lipolytic bacterial strain on the anaerobic digestion of restaurant lipid-rich waste was studied in batch experiments with a model waste containing 10% lipids (triolein) under two sets of experimental conditions: (A) methanogenic conditions, and (B) initially acidogenic conditions in the presence of only the lipolytic strain biomass (4 days), followe

Growth, age at menarche and spontaneous GH secretion were studied in girls after treatment for acute lymphoblastic leukemia (ALL). These girls had normal prepubertal growth but subnormal pubertal growth. Mean final height was 1 SD less than expected before puberty. The average age at menarche was significantly lower than the normal mean for Swedish girls. The mean 24-hour GH secretion was severely

Solution phase synthesis of a constrained Leu(5)-enkephalin amide analogue 10 is reported, in which the cyclic ferrocenyl containing subunit 7 was introduced as a mimetic of the tetrapeptide Tyr-Gly-Gly-Phe unit. Temperature dependence of the chemical shift of the amide protons of 10 indicated a hydrogen bond between the same amino acid residues as observed for the natural Leu-enkepalin in the sin

Objective. To validate self-reported smoking habits in smoking pregnant women and estimate the prevalence of substantial exposure to passive smoking in non-smoking pregnant women. Design. Retrospective, quantitative study, consecutively collected samples. Setting. One antenatal clinic in Blekinge County, Sweden. Subjects. 509 pregnant women. Method. Information about smoking habits were taken from

An account of the electronic structure of AmF3 and AmCl3 has been obtained by Complete Active Space calculations (CASSCF and CASPT2) using either a scalar Douglas-Kroll-Hess Hamiltonian or a relativistic effective core potential. It has been compared to the description obtained by density functional theory (DFT) methods combined with a quasi-relativistic ZORA approach, either in the scalar or two-

An assessment of impacts on Arctic terrestrial ecosystems has emphasized geographical variability in responses of species and ecosystems to environmental change. This variability is usually associated with north-south gradients in climate, biodiversity, vegetation zones, and ecosystem structure and function. It is clear, however, that significant east-west variability in environment, ecosystem str

We present new results for the inner valence levels of clusters of the three inert gases Ar, Kr and Xe based on photoelectron spectroscopy studies. The inner valence levels are compared to the localised core levels and to the delocalised outer valence levels. This comparison shows a gradual change from a relatively localised behaviour for Ar inner valence 3s, over the intermediate case of Kr inner